Touboul Arrhythmogenic Right Ventricular Cardiomyopathy

Although first reported several decades ago, the combination of ventricular tachyarrhythmias and right ventricular diseases only triggered distinctive attention in recent years. This book covers the whole spectrum of arrhythmogenic right ventricular cardiomyopathies. The reader will find the basic information about the anatomical substrate, the pathophysiologic mechanisms, and the clinical forms. A careful review of the diagnostic tests tackles the numerous available options ranging from the traditional electrocardiogram to the most recent imaging techniques. Also discussed are the therapeutic tools, including drugs, and the nonpharmacologic approaches. With clarifying illustrations, in color when necessary, this book serves not only the specialists in arrhythmias, but cardiologists in general.

Foreword. A. John Camm. Editor's Preface. A. John Camm. Authors Preface. Introduction. Definition. Epidemiology. Pathology. Macroscopic Aspect. Histopathology. Limits of Pathologic Diagnosis. Pathogenesis. Clinical Presentations. Ventricular Rhythm Disorders. Ventricular Ectopies/Tachycardia. Sudden Death Due to Ventricular Fibrillation. Other Arrhythmic Events. Heart Failure. Chest Pain. Latent Forms. Diagnostic Tools. Physical Examination. Chest X-Ray. ECG in Sinus Rhythm. Exercise Stress Test. Signal Averaged ECG. Isoproterenol Testing. Electrophysiologic Study. Electrocardiographic Findings. Endomyocardial Biopsy. Right Contrast Ventriculography. Radionuclide Angiography and Computed Tomography. 123I-Meta-Iodobenzylguanidine. Magnetic Resonance Imaging. Genetics. Clinical Approach to ARVC. Differential Diagnosis. Right Ventricular Outflow Tract Tachycardia. Uhl's Disease. Brugada Syndrom. Generalized Cardiomyopathy. Natural History and Prognosis. Therapy. Pharmacologic Therapy. Radiofrequency Catheter Ablation. Surgical Disconnection of the Right Ventricle. Internal Cardioverter-Defibrillator. Treatment of ARVC Associated with Right or Biventricular Heart Failure. Prevention. International Registry. Conclusion. References. Indexes